E-ISSN: 2619-9467

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Year 1993 - Volume 3 - Issue 4

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A Case of McCune-Albright Syndrome
Bir Mccune-Albrıght Sendromu Olgusu

  
Turkiye Klinikleri J Gynecol Obst. 1993;3(4):286-8

Article Language: TR
Copyright Ⓒ 2020 by Türkiye Klinikleri. This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/)
ÖZET
Üç yaşında vajinal kanama şikayeti ile başvuran bir McCune-Albright sendromu olgusu sunuldu. Ciltte yaygın pigmente alanlar mevcut olup, iskelet grafilerinde fibröz displazi bulguları yoktu. Pelvik ultrasonografide sağ overde 33 mm çapında follikül kisti görüldü. Düşük gonadotropinlere rağmen östradiol değeri yüksekti. Olgumuzda akromegali, hipertiroidizm, Cushing sendromu ve hiperparatiroidizm gibi diğer endokrin organların hiperfonksiyon bulguları gözlenmedi. Testolactone tedavisi ile ovarian kistler kayboldu ve vajinal kanamaları azaldı.
ABSTRACT
We presented a 3-year-old girl McCune-Albright syndrome. She had the episodes of vaginal bleeding and scattered cutaneous pigmentations. Radiologic investigations revealed no evidence of polyostotic fibrous displasia. On pelvic ultrasonographic examination a follicle cyst 33 mm in diameter was seen in the right ovary. The values of estradiol was high, despite low levels of gonadotropins. The findings of hyperfunction of other endocrine glands such as acromegaly, hyperthyroidism, Cushing syndrome and hyperparathyroidism were not observed in our patient. The ovarian cysts was disappeared and the episodes of vaginal bleeding reduced during testolactone treatment.